Proximal type epithelioid sarcoma of the vulva

Authors

  • Duly Torres-Cepeda Especialista en Ginecología y Obstetricia, Servicio de Obstetricia y Ginecología, Hospital Central “Dr. Urquinaona”
  • Martha Rondon-Tapia Especialista en Ginecología y Obstetricia, Servicio de Obstetricia y Ginecología, Hospital Central “Dr. Urquinaona”
  • Eduardo Reyna-Villasmil Especialista en Ginecología y Obstetricia, Servicio de Obstetricia y Ginecología, Hospital Central “Dr. Urquinaona”

DOI:

https://doi.org/10.31403/rpgo.v68i2420

Keywords:

Vulva, Sarcoma epitelioide, Neoplasia de la vulva

Abstract

Epithelioid sarcoma is a rare type of mesenchymal tumor. Proximal-type epithelioid
sarcoma of the vulva is an extremely rare malignant tumor of the soft tissues with
frequent recurrences due to its aggressive behaviour. Because its characteristics
are similar to other benign lesions, this leads to diagnostic and therapeutic delays.
Histologic features of this tumor include prominent epithelioid cells and the
appearance of rhabdoid features with marked nuclear atypia. Due to its low incidence,
there are no evidence-based diagnostic algorithms or published recommendations
for treatment. The prognosis is generally poor. A case of proximal type epithelioid
sarcoma of the vulva is presented.

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Revista peruana de ginecología y obstetricia

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Published

2022-07-06

Issue

Vol. 68 No. 2 (2022)

Section

Casos Clínicos

License

Copyright (c) 2022 Duly Torres-Cepeda, Martha Rondon-Tapia, Eduardo Reyna-Villasmil

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

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